Case Report and Review of the Literature: Fatal Reversible Cerebral Vasoconstriction Syndrome

Background: A fatal outcome occurs in 2% of patients with Reversible Cerebral Vasoconstriction Syndrome (RCVS). Due to its rarity, guidelines for the management most severe forms RCVS are lacking. Case presentation: Here, we describe case a 55 year-old woman who died from complications and reviewed reported literature. In our patient, first episode neurological deterioration was preceded by an increase cerebral blood flow velocities assessed transcranial Doppler. evolution could not be prevented despite therapeutic escalation consisting multiple non-invasive invasive treatments including cervical sympathetic bloc continuous arterial infusion nimodipine at site vasoconstriction. Conclusion: This review literature illustrate challenges RCVS. We here how monitoring might help anticipate clinical worsening beginning disease propose novel strategies based on neurophysiological parameters.